Imaging of Renal Angiomyolipomatosis
Main Article Content
Keywords
angiomyolipoma, lymphangioleiomyomatosis, PEComa, renal angiomyolipomatosis, tuberous sclerosis
Abstract
Angiomyolipoma is a type of benign renal tumor. It is sporadic and isolated in 80% of cases. The remaining 20% is associated with tuberous sclerosis complex or pulmonary lymphangioleiomyomatosis. Generally, angiomyolipomas manifest themselves as angiomyolipomatosis, in which the angiomyolipomas are larger, bilateral, and widespread. Understanding whether angiomyolipomas are present in the context of angiomyolipomatosis is of considerable importance because it might be associated with malignant lesions. This article provides an overview of the radiological features of renal angiomyolipomatosis under different imaging techniques such as ultrasound, computed tomography, and magnetic resonance.
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10. Flum AS, Hamoui N, Said MA, Yang XJ, Casalino DD, McGuire BB, et al. Update on the diagnosis and management of renal angiomyolipoma. J Urol. 2016 Apr;195(4 Pt 1):834–46. https://doi.org/10.1016/j.juro.2015.07.126
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12. Halpenny D, Snow A, McNeill G, Torreggiani WC. The radiological diagnosis and treatment of renal angiomyolipoma-current status. Clin Radiol. 2010 Feb;65(2):99–108. https://doi.org/10.1016/j.crad.2009.09.014
13. Logue LG, Acker RE, Sienko AE. Best cases from the AFIP: Angiomyolipomas in tuberous sclerosis. Radiographics. 2003 Jan–Feb;23(1):241–6. https://doi.org/10.1148/rg.231025109
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Nov 14, 2018
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Imaging of Renal Angiomyolipomatosis. (2018). Journal of Renal and Hepatic Disorders, 2(2), 10-19. https://doi.org/10.15586/jrenhep.2018.37
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Review Nephrology
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